Aromatic amino acid hydroxylase enzymes: It works by increasing tolerance to phenylalanine and follow with the advised PKU diet chart.

Sapropterin

Always talk to your provider before starting anything.

Follow PKU diet

• Patients suffering from PKU are advised to follow a specific diet chart prescribed by doctor.
• Diet chart varies according to age and phenyl alanine level in blood.
• The goal is to limit the consumption of phenyl alanine containing foods (protein foods like eggs, cheese, nuts, meat) to prevent its accumulation.
• A special nutritional supplement called PKU formula is available to make sure essential proteins are obtained without PKU.

Since PKU diets vary from person to person the diet chart should be strictly followed as advised by doctor as It will help in maintaining proper nutritious diet

Foods to eat:

• Infants suffering from PKU have to take Lofenalac, a special formula while breast feeding

Foods to avoid:

• Limit the intake of food containing phenylalanine
• Foods that are rich in protein like milk, cheese, nuts, chicken, beef, eggs and fish should be avoided